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1、毛細胞型星形細胞瘤的臨床病理特征的臨床研究呂晶1王成鑫2陳瓊霞2劉麗江2通訊作者1.長江航運總醫(yī)院武漢腦科醫(yī)院病理科湖北武漢430000;2.江大病理診斷所組織病理診斷室湖北武漢430053【摘要】目的:探討毛細胞型星形細胞瘤的臨床病理特征。方法:回顧性分析2例毛細胞型星形細胞瘤患者的臨床資料。結(jié)果:木組2例均為男性,年齡分別為1歲及2歲。發(fā)病部位位于右側(cè)小腦和后顱窩。木組例1鏡下具有雙相性的特點,由比例不等的致密1X(含Rosenthal纖維)和疏松1X(嗜酸性顆粒小體>相互交替組成,腫瘤細胞呈梭形,有毛發(fā)樣的突起的特點。例2鏡下于大量粘液背景中見雙極性的梭形細胞,未見Rosenthal纖
2、維,其內(nèi)血管增生。免疫標(biāo)記顯示,2例瘤細胞均陽性表達膠質(zhì)纖維酸性蛋白(GFAP)、Vimentin蛋白(Vimentin)及S-100蛋白(S-100),而神經(jīng)元特異性烯醇化酶(NSE)只在例1的瘤細胞中表達,2例Ki-67陽性率均<l%。結(jié)論:毛細胞型星形細胞瘤病理上分為毛細胞型星形細胞瘤和毛細胞粘液樣型星形細胞瘤,均好發(fā)于兒童和青少年。毛細胞型星形細胞瘤的組織學(xué)特征是雙相型,含有Rosenthal纖維和嗜酸性小體成分。毛細胞粘液樣型星形細胞瘤是由雙極性的梭形細胞組成,間質(zhì)內(nèi)含宥大量的黏液?!娟P(guān)鍵詞】毛細胞型星形細胞瘤;臨床病理;毛細胞粘液樣型星形細胞瘤【中圖分類號1R739.4【文
3、獻標(biāo)識碼】B【文章編號】1674-8999(2015)8-0274-03Clinicopathologicalfeatuersofpilocyticastrocytoma(reportof2cases)LVJingl,WANGCheng-Xing2,CHENQiong-Xia2,LIULi-Jiang2(1.GeneralHospitaloftheYangtzeRiverShippingWuhanBrainHospital,Wuhan430000,China;2.PathologicaldiagnosisofJianghanUniversity,Wuhan430053,China;)[Abs
4、tract]Objective:ToexploretheClinicopathologicalfeatuersofpilocyticastrocytomas.Methods:Theclinicaldataoftwopilocyticastrocytomaspatientswereanalyzedretrospectively.Results:Allthe2casesoccurredinmalepatientsattheageof1yearsand2yearsrespectively.Exampleonewaslocatedinthethirdcerebellar,whileexampletw
5、owaslocatedattheposteriorfossa.Histologically,intheonecase,thetumorwascomposedofbiphasicpatterncells.Pilocyticastrocytomacharacteristicallycontainedalternativedenselypackedareas(containrosenthalfibers)andlooselypackedarea(containeosinophilicbody).Thetumorcellshavefusiformshapeandhair-likeprojection
6、s.Histologically,seealotofmucusinthebackgroundofbipolarspindlecells,norosenthalfiber.Thereareinnervascularproliferation.Inthetowcases,immunohistochemicalshowedglialfibrillaryacidicprotein(GFAP),Vimentinprotein(Vimentin)andS-100protein(S-100)inneoplasticcellwerepositivity.Butneuronspecificenolase(NS
7、E)expressionintheonecase.ThepositiverateofKi-67nuclearwas1%inneoplasticcell.Conclusions:Histologically,pilocyticastrocytomawascompsedofpilocyticastrocytomasandpilomyxoidastrocytoma.Thetwotypesofpilocyticast